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Updated: Jan 16, 2026

Forskolin-induced Swelling in Intestinal Organoids: An In Vitro Assay for Assessing Drug Response in Cystic Fibrosis Patients
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Treatment with CFTR Modulators for Cystic Fibrosis: What a Pediatric Gastroenterologist Needs to Know

David Gonzalez Jimenez1, Ruth García Romero2, Alejandro Rodríguez Martínez3

  • 1Cystic Fibrosis Unit, Hospital Universitario Central de Asturias, 33011 Oviedo, Spain.

Children (Basel, Switzerland)
|September 27, 2025
PubMed
Summary

CFTR modulators improve gastrointestinal and nutritional health in cystic fibrosis patients. Pediatric gastroenterologists must monitor digestive and bone health outcomes with these new therapies.

Keywords:
CFBDCFLDCFTR modulatorsETIcystic fibrosiscystic fibrosis liver diseasecystic fibrosis-related bone diseasenutritional assessment

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