Right-sided juxtaposition of the atrial appendages in an anencephalic

A case of the uncommon right-sided juxtaposition of the atrial appendages is presented--to our knowledge the 17th instance reported so far. The interest of this case resides in the fact that there were no associated major cardiac anomalies, and that it occurred in an anencephalic female. It is the second reported case of this association. Both cases had in common the presence of ventricular D-looping, normal relationships of the great arteries and only minor cardiac defects. The absence of major cardiac anomalies, in contrast to the more common left-sided juxtaposition, and the association with anencephaly which has not yet been reported in the left-sided variant of juxtaposition, are features which have to be emphasised.