[Gottron's erythroderma congenitalis progressiva symmetrica]

Two patients with erythrokeratoderma are observed, a mother aged 42 and her 16-year-old son. In both cases the dermatosis started on the 40th day after birth and covered slowly and symmetrically the lower and upper limbs as well as the face. The two patients underwent two different treatments: the mother was treated with aromatic retinoid for 8 weeks; the son with PUVA therapy for a total of 63 J/cm2 UVA. With both methods it was possible to obtain good results. However, the results were better with PUVA therapy.