Tricuspid atresia associated with double-orifice mitral valve and coronary sinus septal defect

I S Park1, S J Yoo, K S Kim

  • 1Department of Pediatrics and Radiology, Asan Medical Center, Ulsan University Medical School, Seoul, Korea.

Insights

This case report details a rare cardiac malformation including tricuspid atresia, coronary sinus septal defect, and double-orifice mitral valve. Echocardiography and angiocardiography were used for accurate diagnosis of these complex congenital heart defects.

Area of Science:

  • Cardiology
  • Medical Diagnostics
  • Congenital Heart Disease

Background:

  • Cardiac malformations are complex structural abnormalities present at birth.
  • Rare combinations of congenital heart defects pose diagnostic challenges.
  • Accurate diagnosis is crucial for appropriate patient management.

Purpose of the Study:

  • To present a rare case of complex cardiac malformation.
  • To highlight the diagnostic utility of echocardiography and angiocardiography.
  • To document the specific features of tricuspid atresia, coronary sinus septal defect, and double-orifice mitral valve.

Main Methods:

  • Case presentation of a patient with cardiac malformation.
  • Diagnostic imaging using echocardiography.
  • Confirmatory imaging with angiocardiography.

Main Results:

  • Identification of a rare combination of cardiac defects: tricuspid atresia, coronary sinus septal defect, and double-orifice mitral valve.
  • Successful diagnosis of these anomalies using echocardiography.
  • Confirmation of the diagnosis through angiocardiography.

Conclusions:

  • Echocardiography is a valuable tool for diagnosing complex congenital heart defects.
  • Angiocardiography provides definitive confirmation of cardiac anomalies.
  • This case underscores the importance of comprehensive diagnostic approaches for rare cardiac malformations.

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