Ascites secondary to indolent pacemaker infection in a Fontan patient

This report describes what we believe is the 1st reported case of indolent pacemaker infection's causing abdominal ascites in a patient who has undergone a Fontan operation. Abdominal ascites in a Fontan patient is commonly due to protein-losing enteropathy, systemic venous thrombosis, myocardial dysfunction, chylous ascites, liver cirrhosis, or pancreatitis. Our patient, who had a functional single ventricle, presented with ascites 3 years after undergoing the Fontan operation and pacemaker implantation. After extensive testing and evaluation, we attributed the ascites to indolent infection of the abdominal pacemaker.