Giant left circumflex coronary artery aneurysm with fistula to the right atrium

Jerrold Spapen1, Katrien Van Kolen1, Arno Gigase1

  • 1a Hartcentrum ZNA , Middelheim Hospital , Antwerp , Belgium.

Acta Cardiologica
|July 27, 2017
PubMed

Insights

Coronary artery fistulae are rare congenital heart defects. This case highlights an unusual presentation involving giant aneurysms of the circumflex artery with a fistula to the right atrium.

Area of Science:

  • Cardiology
  • Cardiac Surgery
  • Medical Imaging

Background:

  • Coronary artery fistulae (CAF) are uncommon congenital or acquired abnormal connections between a coronary artery and a heart chamber or great vessel.
  • Prevalence is approximately 0.2% in patients undergoing coronary angiography, with most originating from the right coronary artery.
  • While often asymptomatic, CAFs can lead to significant complications such as angina, heart failure, and arrhythmias.

Observation:

  • We report a rare case of a patient with a significantly dilated circumflex coronary artery.
  • The circumflex artery exhibited two giant aneurysms.
  • A fistulous tract directly connected the aneurysms to the right atrium.

Findings:

  • This unusual anatomy presented a unique challenge for diagnosis and potential management.
  • The large aneurysms and direct right atrial communication represent a rare variant of coronary artery fistula.
  • Detailed imaging was crucial for delineating the complex fistulous pathways.

Implications:

  • This case underscores the importance of recognizing diverse presentations of coronary artery anomalies.
  • Understanding such rare anatomies is vital for surgical planning and patient outcomes.
  • Further research into the natural history and management of giant coronary aneurysms with fistulae is warranted.

Related Concept Videos

Coronary Circulation01:21

Coronary Circulation

The heart, an organ critical to survival, gets nourishment not from the blood it pumps but from a separate circulation system known as coronary circulation. This is the shortest circulation in the body and is responsible for supplying the heart with the nutrients it needs to function effectively.
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
7.9K
Chambers of the Heart01:16

Chambers of the Heart

The human heart is a complex organ made up of four chambers: the right and left atria and the right and left ventricles. These internal chambers are separated by partitions known as the interatrial and interventricular septa. The exterior of the heart features a groove known as the coronary sulcus that demarcates the atria from the ventricles, while the anterior and posterior interventricular sulci distinguish between the two ventricles.
Deoxygenated blood from the body is received in the right...
10.8K
Aortic Regurgitation II: Clinical Features and Diagnostic Tests01:22

Aortic Regurgitation II: Clinical Features and Diagnostic Tests

Aortic valve regurgitation (AR) occurs when the aortic valve fails to close properly, allowing blood to flow backward from the aorta into the left ventricle. This backflow can result in two distinct clinical presentations: acute and chronic AR, each characterized by its own set of symptoms and physical findings.Acute Aortic RegurgitationAcute AR presents with a sudden onset of severe symptoms. Patients typically experience profound dyspnea (shortness of breath), chest pain, and signs of left...
659
The Aorta01:14

The Aorta

The aorta is the largest artery in the human body. It originates from the left ventricle of the heart and extends down to the abdomen, where it splits into two smaller arteries. Structurally, it can be divided into four main parts: the ascending aorta, the aortic arch, the thoracic aorta, and the abdominal aorta.
The average diameter of the aorta is approximately 2-3 cm, but the size can vary depending on the section of the aorta and the individual's age, sex, and body size. The aorta is...
3.3K
Cardiac Catheterization III: Left Heart Catheterization01:24

Cardiac Catheterization III: Left Heart Catheterization

Left heart catheterization is an invasive diagnostic procedure used to evaluate the function and structure of the left side of the heart. It is generally performed to diagnose and treat cardiovascular conditions such as valve abnormalities, coronary artery disease, and congenital heart defects.Diagnostic and therapeutic purposesLeft heart catheterization serves various diagnostic and therapeutic purposes, including:Assessing coronary artery bypass grafts.Evaluating coronary artery disease in...
877
Aneurysm I: Introduction01:30

Aneurysm I: Introduction

An aortic aneurysm is a localized outpouching or dilation at a weak point in the artery wall. It may involve different parts of the aorta, such as the abdominal aorta, aortic arch, or thoracic aorta.Etiological factorsSeveral disorders are associated with aortic aneurysms.Congenital causes, such as primary connective tissue disorders like Marfan syndrome, impact the integrity and strength of connective tissues, notably affecting the aorta. Marfan syndrome is a genetic disorder that specifically...
542