Giant left circumflex coronary artery aneurysm with fistula to the right atrium
Jerrold Spapen1, Katrien Van Kolen1, Arno Gigase1
1a Hartcentrum ZNA , Middelheim Hospital , Antwerp , Belgium.
Insights
Coronary artery fistulae are rare congenital heart defects. This case highlights an unusual presentation involving giant aneurysms of the circumflex artery with a fistula to the right atrium.
Area of Science:
- Cardiology
- Cardiac Surgery
- Medical Imaging
Background:
- Coronary artery fistulae (CAF) are uncommon congenital or acquired abnormal connections between a coronary artery and a heart chamber or great vessel.
- Prevalence is approximately 0.2% in patients undergoing coronary angiography, with most originating from the right coronary artery.
- While often asymptomatic, CAFs can lead to significant complications such as angina, heart failure, and arrhythmias.
Observation:
- We report a rare case of a patient with a significantly dilated circumflex coronary artery.
- The circumflex artery exhibited two giant aneurysms.
- A fistulous tract directly connected the aneurysms to the right atrium.
Findings:
- This unusual anatomy presented a unique challenge for diagnosis and potential management.
- The large aneurysms and direct right atrial communication represent a rare variant of coronary artery fistula.
- Detailed imaging was crucial for delineating the complex fistulous pathways.
Implications:
- This case underscores the importance of recognizing diverse presentations of coronary artery anomalies.
- Understanding such rare anatomies is vital for surgical planning and patient outcomes.
- Further research into the natural history and management of giant coronary aneurysms with fistulae is warranted.
Abstract:
Coronary artery fistulae are rare cardiac anomalies with a prevalence of 0.2% of all the patients undergoing coronary angiography. The majority of them are congenital and generally origin from the right coronary artery. Occasionally acquired (mostly iatrogenic) fistulae can develop. Although frequently subclinical, symptoms of angina and congestive heart failure may occur. We present an unusual well-illustrated case of a strongly dilated circumflex coronary artery with formation of two giant aneurysms and fistulous communication towards the right atrium.
Related Concept Videos
Coronary Circulation
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
Chambers of the Heart
Deoxygenated blood from the body is received in the right...
Aortic Regurgitation II: Clinical Features and Diagnostic Tests
The Aorta
The average diameter of the aorta is approximately 2-3 cm, but the size can vary depending on the section of the aorta and the individual's age, sex, and body size. The aorta is...
Cardiac Catheterization III: Left Heart Catheterization
Aneurysm I: Introduction


